This Article Full Text Full Text (PDF) Alert me when this article is cited Alert me if a correction is posted Citation Map Services Email this article to a friend Similar articles in this journal Similar articles in PubMed Alert me to new issues of the journal Add to Personal Folders Download to citation manager Author home page(s): Pradeep Narayan Hazaim Alwair Alan J. Bryan Permission Requests Citing Articles Citing Articles via HighWire Citing Articles via Google Scholar Google Scholar Articles by Narayan, P. Articles by Bryan, A. J. Search for Related Content PubMed PubMed Citation Articles by Narayan, P. Articles by Bryan, A. J. Related Collections Great vessels

Surgical resection of sequential thoracic aortic aneurysms in Wiskott–Aldrich syndrome

Department of Cardio-thoracic Surgery, Bristol Royal Infirmary, Bristol Heart Institute, Bristol BS2 8HW, UK

^* Corresponding author. Tel.: +44-11-79-28-5151; fax: +44-11-79-28-51-92
alan.bryan{at}ubht.swest.nhs.uk

Wiskott–Aldrich syndrome is a rare X-linked disorder. Vasculitis and aneurysm formation are extremely rare but potentially fatal complications of the disease. Aortitis and aneurysm formation seem to be progressive in patients with Wiskott–Aldrich syndrome. The risk of death from aneurysmal rupture in patients with Wiskott–Aldrich syndrome is high and hence surgery is required for resection of aneurysms. We report a case where a successful resection of a descending thoracic aneurysm was carried out in a patient who previously had undergone a composite root replacement for aortic root dilatation.

Key Words: Wiskott–Aldrich syndrome; Aortic surgery; Surgical resection

This article has been cited by other articles:

				E. Bernabeu, M. Josa, B. Nomdedeu, J. Ramirez, A. Garcia-Valentin, C. A. Mestres, and J. Mulet One-Step Surgical Approach of a Thoracic Aortic Aneurysm in Wiskott-Aldrich Syndrome Ann. Thorac. Surg., April 1, 2007; 83(4): 1537 - 1538. [Abstract] [Full Text] [PDF]